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KMID : 0356920090560060717
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Korean Journal of Anesthesiology
2009 Volume.56 No. 6 p.717 ~ p.719
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Anesthetic experience of a pediatric patient with Seckel syndrome associated with pneumonia -A case report-
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Kim Tae-Hee
Hwang Jai-Hyun
Song Jun-Gol
Kim Young-Uk
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Abstract
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Seckel syndrome, also called bird-headed dwarfism, is an extremely rare, inherited, autosomal recessive disorder. The patients with Seckel syndrome are characterized by growth retardation, microcephaly with mental retardation, proportional dwarfism, bird like faces, and beak-like triangular nose. A literature review reveals that they have multiple anesthetic problems such as difficult airway management, difficult venous cannulation and concomitant medical diseases. We describe our experience in anesthetic management of a 21-month-old male patient with Seckel syndrome associated with pneumonia who underwent orchiopexy for bilateral cryptochidism.
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KEYWORD
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Airway management, Bird-headed dwarfism, Seckel syndrome
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